Data Exchange Profiles for 2022 CDC Clinical Practice Guideline for Prescribing Opioids
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: Sickle-cell diseases - XML Representation

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<ValueSet xmlns="http://hl7.org/fhir">
  <id value="sickle-cell-diseases"/>
  <meta>
    <profile
             value="http://hl7.org/fhir/uv/crmi/StructureDefinition/crmi-expandedvalueset"/>
  </meta>
  <text>
    <status value="generated"/>
    <div xmlns="http://www.w3.org/1999/xhtml"><p class="res-header-id"><b>Generated Narrative: ValueSet sickle-cell-diseases</b></p><a name="sickle-cell-diseases"> </a><a name="hcsickle-cell-diseases"> </a><div style="display: inline-block; background-color: #d9e0e7; padding: 6px; margin: 4px; border: 1px solid #8da1b4; border-radius: 5px; line-height: 60%"><p style="margin-bottom: 0px"/><p style="margin-bottom: 0px">Profile: <a href="http://hl7.org/fhir/uv/crmi/STU1/StructureDefinition-crmi-expandedvalueset.html">CRMI Expanded ValueSet</a></p></div><p>This value set expansion contains 81 concepts.</p><table class="codes"><tr><td style="white-space:nowrap"><b>Code</b></td><td><b>System</b></td><td><b>Display</b></td></tr><tr><td style="white-space:nowrap"><a name="sickle-cell-diseases-http://snomed.info/sct-417357006"> </a>  <a href="http://snomed.info/id/417357006">417357006</a></td><td>http://snomed.info/sct</td><td>Sickling disorder due to hemoglobin S (disorder)</td></tr><tr><td style="white-space:nowrap"><a name="sickle-cell-diseases-http://snomed.info/sct-23269001"> </a>  <a href="http://snomed.info/id/23269001">23269001</a></td><td>http://snomed.info/sct</td><td>Double heterozygous sickling disorder</td></tr><tr><td style="white-space:nowrap"><a name="sickle-cell-diseases-http://snomed.info/sct-25472008"> </a>  <a href="http://snomed.info/id/25472008">25472008</a></td><td>http://snomed.info/sct</td><td>Sickle cell-hemoglobin D disease</td></tr><tr><td style="white-space:nowrap"><a name="sickle-cell-diseases-http://snomed.info/sct-35434009"> </a>  <a href="http://snomed.info/id/35434009">35434009</a></td><td>http://snomed.info/sct</td><td>Sickle cell-hemoglobin C disease</td></tr><tr><td style="white-space:nowrap"><a name="sickle-cell-diseases-http://snomed.info/sct-36472007"> </a>  <a href="http://snomed.info/id/36472007">36472007</a></td><td>http://snomed.info/sct</td><td>Hemoglobin S-F disease</td></tr><tr><td style="white-space:nowrap"><a name="sickle-cell-diseases-http://snomed.info/sct-47024008"> </a>  <a href="http://snomed.info/id/47024008">47024008</a></td><td>http://snomed.info/sct</td><td>Sickle cell-hemoglobin E disease</td></tr><tr><td style="white-space:nowrap"><a name="sickle-cell-diseases-http://snomed.info/sct-127040003"> </a>  <a href="http://snomed.info/id/127040003">127040003</a></td><td>http://snomed.info/sct</td><td>Sickle cell anemia</td></tr><tr><td style="white-space:nowrap"><a name="sickle-cell-diseases-http://snomed.info/sct-127041004"> </a>  <a href="http://snomed.info/id/127041004">127041004</a></td><td>http://snomed.info/sct</td><td>Sickle cell-beta-thalassemia</td></tr><tr><td style="white-space:nowrap"><a name="sickle-cell-diseases-http://snomed.info/sct-127042006"> </a>  <a href="http://snomed.info/id/127042006">127042006</a></td><td>http://snomed.info/sct</td><td>Sickle cell beta plus thalassaemia</td></tr><tr><td style="white-space:nowrap"><a name="sickle-cell-diseases-http://snomed.info/sct-127043001"> </a>  <a href="http://snomed.info/id/127043001">127043001</a></td><td>http://snomed.info/sct</td><td>Sickle cell-beta^0^-thalassemia</td></tr><tr><td style="white-space:nowrap"><a name="sickle-cell-diseases-http://snomed.info/sct-127044007"> </a>  <a href="http://snomed.info/id/127044007">127044007</a></td><td>http://snomed.info/sct</td><td>Sickle cell-delta beta^0^-thalassemia</td></tr><tr><td style="white-space:nowrap"><a name="sickle-cell-diseases-http://snomed.info/sct-127045008"> </a>  <a href="http://snomed.info/id/127045008">127045008</a></td><td>http://snomed.info/sct</td><td>Sickle cell anemia with coexistent alpha-thalassemia</td></tr><tr><td style="white-space:nowrap"><a name="sickle-cell-diseases-http://snomed.info/sct-127047000"> </a>  <a href="http://snomed.info/id/127047000">127047000</a></td><td>http://snomed.info/sct</td><td>Sickle cell-hemoglobin Lepore disease</td></tr><tr><td style="white-space:nowrap"><a name="sickle-cell-diseases-http://snomed.info/sct-127048005"> </a>  <a href="http://snomed.info/id/127048005">127048005</a></td><td>http://snomed.info/sct</td><td>Sickle cell-Hemoglobin O Arab disease</td></tr><tr><td style="white-space:nowrap"><a name="sickle-cell-diseases-http://snomed.info/sct-234391009"> </a>  <a href="http://snomed.info/id/234391009">234391009</a></td><td>http://snomed.info/sct</td><td>Sickle cell anemia with high hemoglobin F</td></tr><tr><td style="white-space:nowrap"><a name="sickle-cell-diseases-http://snomed.info/sct-416484003"> </a>  <a href="http://snomed.info/id/416484003">416484003</a></td><td>http://snomed.info/sct</td><td>Sickle cell-hemoglobin E disease with crisis (disorder)</td></tr><tr><td style="white-space:nowrap"><a name="sickle-cell-diseases-http://snomed.info/sct-416826005"> </a>  <a href="http://snomed.info/id/416826005">416826005</a></td><td>http://snomed.info/sct</td><td>Sickle cell-thalassemia disease with crisis (disorder)</td></tr><tr><td style="white-space:nowrap"><a name="sickle-cell-diseases-http://snomed.info/sct-417048006"> </a>  <a href="http://snomed.info/id/417048006">417048006</a></td><td>http://snomed.info/sct</td><td>Sickle cell-thalassemia disease without crisis (disorder)</td></tr><tr><td style="white-space:nowrap"><a name="sickle-cell-diseases-http://snomed.info/sct-417279003"> </a>  <a href="http://snomed.info/id/417279003">417279003</a></td><td>http://snomed.info/sct</td><td>Hemoglobin S sickling disorder with crisis (disorder)</td></tr><tr><td style="white-space:nowrap"><a name="sickle-cell-diseases-http://snomed.info/sct-417425009"> </a>  <a href="http://snomed.info/id/417425009">417425009</a></td><td>http://snomed.info/sct</td><td>Hemoglobin SS disease with crisis (disorder)</td></tr><tr><td style="white-space:nowrap"><a name="sickle-cell-diseases-http://snomed.info/sct-417517009"> </a>  <a href="http://snomed.info/id/417517009">417517009</a></td><td>http://snomed.info/sct</td><td>Sickle cell-hemoglobin C disease with crisis (disorder)</td></tr><tr><td style="white-space:nowrap"><a name="sickle-cell-diseases-http://snomed.info/sct-417748003"> </a>  <a href="http://snomed.info/id/417748003">417748003</a></td><td>http://snomed.info/sct</td><td>Sickle cell-hemoglobin D disease with crisis (disorder)</td></tr><tr><td style="white-space:nowrap"><a name="sickle-cell-diseases-http://snomed.info/sct-440206000"> </a>  <a href="http://snomed.info/id/440206000">440206000</a></td><td>http://snomed.info/sct</td><td>Hemoglobin SS disease with vasoocclusive crisis (disorder)</td></tr><tr><td style="white-space:nowrap"><a name="sickle-cell-diseases-http://snomed.info/sct-444108000"> </a>  <a href="http://snomed.info/id/444108000">444108000</a></td><td>http://snomed.info/sct</td><td>Acute sickle cell splenic sequestration crisis (disorder)</td></tr><tr><td style="white-space:nowrap"><a name="sickle-cell-diseases-http://snomed.info/sct-783254003"> </a>  <a href="http://snomed.info/id/783254003">783254003</a></td><td>http://snomed.info/sct</td><td>Hereditary persistence of fetal hemoglobin with sickle cell disease syndrome</td></tr><tr><td style="white-space:nowrap"><a name="sickle-cell-diseases-http://snomed.info/sct-1153413001"> </a>  <a href="http://snomed.info/id/1153413001">1153413001</a></td><td>http://snomed.info/sct</td><td>Acute sequestration of spleen due to sickle cell thalassemia with crisis (disorder)</td></tr><tr><td style="white-space:nowrap"><a name="sickle-cell-diseases-http://snomed.info/sct-1153415008"> </a>  <a href="http://snomed.info/id/1153415008">1153415008</a></td><td>http://snomed.info/sct</td><td>Acute splenic sequestration due to sickle cell hemoglobin C disease with crisis</td></tr><tr><td style="white-space:nowrap"><a name="sickle-cell-diseases-http://snomed.info/sct-10759351000119103"> </a>  <a href="http://snomed.info/id/10759351000119103">10759351000119103</a></td><td>http://snomed.info/sct</td><td>Sickle cell anaemia in mother complicating childbirth</td></tr><tr><td style="white-space:nowrap"><a name="sickle-cell-diseases-http://snomed.info/sct-441482006"> </a>  <a href="http://snomed.info/id/441482006">441482006</a></td><td>http://snomed.info/sct</td><td>History of sickle cell anaemia</td></tr><tr><td style="white-space:nowrap"><a name="sickle-cell-diseases-http://hl7.org/fhir/sid/icd-10-cm-D57"> </a>  D57</td><td>http://hl7.org/fhir/sid/icd-10-cm</td><td>Sickle-cell disorders</td></tr><tr><td style="white-space:nowrap"><a name="sickle-cell-diseases-http://hl7.org/fhir/sid/icd-10-cm-D57.0"> </a>  D57.0</td><td>http://hl7.org/fhir/sid/icd-10-cm</td><td>Hb-SS disease with crisis</td></tr><tr><td style="white-space:nowrap"><a name="sickle-cell-diseases-http://hl7.org/fhir/sid/icd-10-cm-D57.00"> </a>  D57.00</td><td>http://hl7.org/fhir/sid/icd-10-cm</td><td>Hb-SS disease with crisis, unspecified</td></tr><tr><td style="white-space:nowrap"><a name="sickle-cell-diseases-http://hl7.org/fhir/sid/icd-10-cm-D57.01"> </a>  D57.01</td><td>http://hl7.org/fhir/sid/icd-10-cm</td><td>Hb-SS disease with acute chest syndrome</td></tr><tr><td style="white-space:nowrap"><a name="sickle-cell-diseases-http://hl7.org/fhir/sid/icd-10-cm-D57.02"> </a>  D57.02</td><td>http://hl7.org/fhir/sid/icd-10-cm</td><td>Hb-SS disease with splenic sequestration</td></tr><tr><td style="white-space:nowrap"><a name="sickle-cell-diseases-http://hl7.org/fhir/sid/icd-10-cm-D57.03"> </a>  D57.03</td><td>http://hl7.org/fhir/sid/icd-10-cm</td><td>Hb-SS disease with cerebral vascular involvement</td></tr><tr><td style="white-space:nowrap"><a name="sickle-cell-diseases-http://hl7.org/fhir/sid/icd-10-cm-D57.04"> </a>  D57.04</td><td>http://hl7.org/fhir/sid/icd-10-cm</td><td>Hb-SS disease with dactylitis</td></tr><tr><td style="white-space:nowrap"><a name="sickle-cell-diseases-http://hl7.org/fhir/sid/icd-10-cm-D57.09"> </a>  D57.09</td><td>http://hl7.org/fhir/sid/icd-10-cm</td><td>Hb-SS disease with crisis with other specified complication</td></tr><tr><td style="white-space:nowrap"><a name="sickle-cell-diseases-http://hl7.org/fhir/sid/icd-10-cm-D57.2"> </a>  D57.2</td><td>http://hl7.org/fhir/sid/icd-10-cm</td><td>Sickle-cell/Hb-C disease</td></tr><tr><td style="white-space:nowrap"><a name="sickle-cell-diseases-http://hl7.org/fhir/sid/icd-10-cm-D57.20"> </a>  D57.20</td><td>http://hl7.org/fhir/sid/icd-10-cm</td><td>Sickle-cell/Hb-C disease without crisis</td></tr><tr><td style="white-space:nowrap"><a name="sickle-cell-diseases-http://hl7.org/fhir/sid/icd-10-cm-D57.21"> </a>  D57.21</td><td>http://hl7.org/fhir/sid/icd-10-cm</td><td>Sickle-cell/Hb-C disease with crisis</td></tr><tr><td style="white-space:nowrap"><a name="sickle-cell-diseases-http://hl7.org/fhir/sid/icd-10-cm-D57.211"> </a>  D57.211</td><td>http://hl7.org/fhir/sid/icd-10-cm</td><td>Sickle-cell/Hb-C disease with acute chest syndrome</td></tr><tr><td style="white-space:nowrap"><a name="sickle-cell-diseases-http://hl7.org/fhir/sid/icd-10-cm-D57.212"> </a>  D57.212</td><td>http://hl7.org/fhir/sid/icd-10-cm</td><td>Sickle-cell/Hb-C disease with splenic sequestration</td></tr><tr><td style="white-space:nowrap"><a name="sickle-cell-diseases-http://hl7.org/fhir/sid/icd-10-cm-D57.213"> </a>  D57.213</td><td>http://hl7.org/fhir/sid/icd-10-cm</td><td>Sickle-cell/Hb-C disease with cerebral vascular involvement</td></tr><tr><td style="white-space:nowrap"><a name="sickle-cell-diseases-http://hl7.org/fhir/sid/icd-10-cm-D57.214"> </a>  D57.214</td><td>http://hl7.org/fhir/sid/icd-10-cm</td><td>Sickle-cell/Hb-C disease with dactylitis</td></tr><tr><td style="white-space:nowrap"><a name="sickle-cell-diseases-http://hl7.org/fhir/sid/icd-10-cm-D57.218"> </a>  D57.218</td><td>http://hl7.org/fhir/sid/icd-10-cm</td><td>Sickle-cell/Hb-C disease with crisis with other specified complication</td></tr><tr><td style="white-space:nowrap"><a name="sickle-cell-diseases-http://hl7.org/fhir/sid/icd-10-cm-D57.219"> </a>  D57.219</td><td>http://hl7.org/fhir/sid/icd-10-cm</td><td>Sickle-cell/Hb-C disease with crisis, unspecified</td></tr><tr><td style="white-space:nowrap"><a name="sickle-cell-diseases-http://hl7.org/fhir/sid/icd-10-cm-D57.3"> </a>  D57.3</td><td>http://hl7.org/fhir/sid/icd-10-cm</td><td>Sickle-cell trait</td></tr><tr><td style="white-space:nowrap"><a name="sickle-cell-diseases-http://hl7.org/fhir/sid/icd-10-cm-D57.4"> </a>  D57.4</td><td>http://hl7.org/fhir/sid/icd-10-cm</td><td>Sickle-cell thalassemia</td></tr><tr><td style="white-space:nowrap"><a name="sickle-cell-diseases-http://hl7.org/fhir/sid/icd-10-cm-D57.40"> </a>  D57.40</td><td>http://hl7.org/fhir/sid/icd-10-cm</td><td>Sickle-cell thalassemia without crisis</td></tr><tr><td style="white-space:nowrap"><a name="sickle-cell-diseases-http://hl7.org/fhir/sid/icd-10-cm-D57.41"> </a>  D57.41</td><td>http://hl7.org/fhir/sid/icd-10-cm</td><td>Sickle-cell thalassemia, unspecified, with crisis</td></tr><tr><td style="white-space:nowrap"><a name="sickle-cell-diseases-http://hl7.org/fhir/sid/icd-10-cm-D57.411"> </a>  D57.411</td><td>http://hl7.org/fhir/sid/icd-10-cm</td><td>Sickle-cell thalassemia, unspecified, with acute chest syndrome</td></tr><tr><td style="white-space:nowrap"><a name="sickle-cell-diseases-http://hl7.org/fhir/sid/icd-10-cm-D57.412"> </a>  D57.412</td><td>http://hl7.org/fhir/sid/icd-10-cm</td><td>Sickle-cell thalassemia, unspecified, with splenic sequestration</td></tr><tr><td style="white-space:nowrap"><a name="sickle-cell-diseases-http://hl7.org/fhir/sid/icd-10-cm-D57.413"> </a>  D57.413</td><td>http://hl7.org/fhir/sid/icd-10-cm</td><td>Sickle-cell thalassemia, unspecified, with cerebral vascular involvement</td></tr><tr><td style="white-space:nowrap"><a name="sickle-cell-diseases-http://hl7.org/fhir/sid/icd-10-cm-D57.414"> </a>  D57.414</td><td>http://hl7.org/fhir/sid/icd-10-cm</td><td>Sickle-cell thalassemia, unspecified, with dactylitis</td></tr><tr><td style="white-space:nowrap"><a name="sickle-cell-diseases-http://hl7.org/fhir/sid/icd-10-cm-D57.418"> </a>  D57.418</td><td>http://hl7.org/fhir/sid/icd-10-cm</td><td>Sickle-cell thalassemia, unspecified, with crisis with other specified complication</td></tr><tr><td style="white-space:nowrap"><a name="sickle-cell-diseases-http://hl7.org/fhir/sid/icd-10-cm-D57.419"> </a>  D57.419</td><td>http://hl7.org/fhir/sid/icd-10-cm</td><td>Sickle-cell thalassemia, unspecified, with crisis</td></tr><tr><td style="white-space:nowrap"><a name="sickle-cell-diseases-http://hl7.org/fhir/sid/icd-10-cm-D57.42"> </a>  D57.42</td><td>http://hl7.org/fhir/sid/icd-10-cm</td><td>Sickle-cell thalassemia beta zero without crisis</td></tr><tr><td style="white-space:nowrap"><a name="sickle-cell-diseases-http://hl7.org/fhir/sid/icd-10-cm-D57.43"> </a>  D57.43</td><td>http://hl7.org/fhir/sid/icd-10-cm</td><td>Sickle-cell thalassemia beta zero with crisis</td></tr><tr><td style="white-space:nowrap"><a name="sickle-cell-diseases-http://hl7.org/fhir/sid/icd-10-cm-D57.431"> </a>  D57.431</td><td>http://hl7.org/fhir/sid/icd-10-cm</td><td>Sickle-cell thalassemia beta zero with acute chest syndrome</td></tr><tr><td style="white-space:nowrap"><a name="sickle-cell-diseases-http://hl7.org/fhir/sid/icd-10-cm-D57.432"> </a>  D57.432</td><td>http://hl7.org/fhir/sid/icd-10-cm</td><td>Sickle-cell thalassemia beta zero with splenic sequestration</td></tr><tr><td style="white-space:nowrap"><a name="sickle-cell-diseases-http://hl7.org/fhir/sid/icd-10-cm-D57.433"> </a>  D57.433</td><td>http://hl7.org/fhir/sid/icd-10-cm</td><td>Sickle-cell thalassemia beta zero with cerebral vascular involvement</td></tr><tr><td style="white-space:nowrap"><a name="sickle-cell-diseases-http://hl7.org/fhir/sid/icd-10-cm-D57.434"> </a>  D57.434</td><td>http://hl7.org/fhir/sid/icd-10-cm</td><td>Sickle-cell thalassemia beta zero with dactylitis</td></tr><tr><td style="white-space:nowrap"><a name="sickle-cell-diseases-http://hl7.org/fhir/sid/icd-10-cm-D57.438"> </a>  D57.438</td><td>http://hl7.org/fhir/sid/icd-10-cm</td><td>Sickle-cell thalassemia beta zero with crisis with other specified complication</td></tr><tr><td style="white-space:nowrap"><a name="sickle-cell-diseases-http://hl7.org/fhir/sid/icd-10-cm-D57.439"> </a>  D57.439</td><td>http://hl7.org/fhir/sid/icd-10-cm</td><td>Sickle-cell thalassemia beta zero with crisis, unspecified</td></tr><tr><td style="white-space:nowrap"><a name="sickle-cell-diseases-http://hl7.org/fhir/sid/icd-10-cm-D57.44"> </a>  D57.44</td><td>http://hl7.org/fhir/sid/icd-10-cm</td><td>Sickle-cell thalassemia beta plus without crisis</td></tr><tr><td style="white-space:nowrap"><a name="sickle-cell-diseases-http://hl7.org/fhir/sid/icd-10-cm-D57.45"> </a>  D57.45</td><td>http://hl7.org/fhir/sid/icd-10-cm</td><td>Sickle-cell thalassemia beta plus with crisis</td></tr><tr><td style="white-space:nowrap"><a name="sickle-cell-diseases-http://hl7.org/fhir/sid/icd-10-cm-D57.451"> </a>  D57.451</td><td>http://hl7.org/fhir/sid/icd-10-cm</td><td>Sickle-cell thalassemia beta plus with acute chest syndrome</td></tr><tr><td style="white-space:nowrap"><a name="sickle-cell-diseases-http://hl7.org/fhir/sid/icd-10-cm-D57.452"> </a>  D57.452</td><td>http://hl7.org/fhir/sid/icd-10-cm</td><td>Sickle-cell thalassemia beta plus with splenic sequestration</td></tr><tr><td style="white-space:nowrap"><a name="sickle-cell-diseases-http://hl7.org/fhir/sid/icd-10-cm-D57.453"> </a>  D57.453</td><td>http://hl7.org/fhir/sid/icd-10-cm</td><td>Sickle-cell thalassemia beta plus with cerebral vascular involvement</td></tr><tr><td style="white-space:nowrap"><a name="sickle-cell-diseases-http://hl7.org/fhir/sid/icd-10-cm-D57.454"> </a>  D57.454</td><td>http://hl7.org/fhir/sid/icd-10-cm</td><td>Sickle-cell thalassemia beta plus with dactylitis</td></tr><tr><td style="white-space:nowrap"><a name="sickle-cell-diseases-http://hl7.org/fhir/sid/icd-10-cm-D57.458"> </a>  D57.458</td><td>http://hl7.org/fhir/sid/icd-10-cm</td><td>Sickle-cell thalassemia beta plus with crisis with other specified complication</td></tr><tr><td style="white-space:nowrap"><a name="sickle-cell-diseases-http://hl7.org/fhir/sid/icd-10-cm-D57.459"> </a>  D57.459</td><td>http://hl7.org/fhir/sid/icd-10-cm</td><td>Sickle-cell thalassemia beta plus with crisis, unspecified</td></tr><tr><td style="white-space:nowrap"><a name="sickle-cell-diseases-http://hl7.org/fhir/sid/icd-10-cm-D57.8"> </a>  D57.8</td><td>http://hl7.org/fhir/sid/icd-10-cm</td><td>Other sickle-cell disorders</td></tr><tr><td style="white-space:nowrap"><a name="sickle-cell-diseases-http://hl7.org/fhir/sid/icd-10-cm-D57.80"> </a>  D57.80</td><td>http://hl7.org/fhir/sid/icd-10-cm</td><td>Other sickle-cell disorders without crisis</td></tr><tr><td style="white-space:nowrap"><a name="sickle-cell-diseases-http://hl7.org/fhir/sid/icd-10-cm-D57.81"> </a>  D57.81</td><td>http://hl7.org/fhir/sid/icd-10-cm</td><td>Other sickle-cell disorders with crisis</td></tr><tr><td style="white-space:nowrap"><a name="sickle-cell-diseases-http://hl7.org/fhir/sid/icd-10-cm-D57.811"> </a>  D57.811</td><td>http://hl7.org/fhir/sid/icd-10-cm</td><td>Other sickle-cell disorders with acute chest syndrome</td></tr><tr><td style="white-space:nowrap"><a name="sickle-cell-diseases-http://hl7.org/fhir/sid/icd-10-cm-D57.812"> </a>  D57.812</td><td>http://hl7.org/fhir/sid/icd-10-cm</td><td>Other sickle-cell disorders with splenic sequestration</td></tr><tr><td style="white-space:nowrap"><a name="sickle-cell-diseases-http://hl7.org/fhir/sid/icd-10-cm-D57.813"> </a>  D57.813</td><td>http://hl7.org/fhir/sid/icd-10-cm</td><td>Other sickle-cell disorders with cerebral vascular involvement</td></tr><tr><td style="white-space:nowrap"><a name="sickle-cell-diseases-http://hl7.org/fhir/sid/icd-10-cm-D57.814"> </a>  D57.814</td><td>http://hl7.org/fhir/sid/icd-10-cm</td><td>Other sickle-cell disorders with dactylitis</td></tr><tr><td style="white-space:nowrap"><a name="sickle-cell-diseases-http://hl7.org/fhir/sid/icd-10-cm-D57.818"> </a>  D57.818</td><td>http://hl7.org/fhir/sid/icd-10-cm</td><td>Other sickle-cell disorders with crisis with other specified complication</td></tr><tr><td style="white-space:nowrap"><a name="sickle-cell-diseases-http://hl7.org/fhir/sid/icd-10-cm-D57.819"> </a>  D57.819</td><td>http://hl7.org/fhir/sid/icd-10-cm</td><td>Other sickle-cell disorders with crisis, unspecified</td></tr></table></div>
  </text>
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    <valueContactDetail>
      <name value="MD Partners, Inc."/>
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        <system value="email"/>
        <value value="info@mdpartners.com"/>
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    <valueMarkdown
                   value="This value set contains a point-in-time expansion enumerating the codes that meet the value set intent. As new versions of the code systems used by the value set are released, the contents of this expansion will need to be updated to incorporate newly defined codes that meet the value set intent. Before, and periodically during production use, the value set expansion contents SHOULD be updated."/>
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  <url
       value="http://fhir.org/guides/cdc/opioid-cds/ValueSet/sickle-cell-diseases"/>
  <version value="1.0.0-ballot"/>
  <name value="SICKLE_CELL_DISEASES"/>
  <title value="Sickle-cell diseases"/>
  <status value="active"/>
  <experimental value="false"/>
  <date value="2023-05-25T18:08:12-06:00"/>
  <publisher value="HL7 International / Clinical Decision Support"/>
  <contact>
    <telecom>
      <system value="url"/>
      <value value="http://www.hl7.org/Special/committees/dss"/>
    </telecom>
  </contact>
  <description value="Sickle-cell disorders that cause painful crisis"/>
  <jurisdiction>
    <coding>
      <system value="urn:iso:std:iso:3166"/>
      <code value="US"/>
    </coding>
  </jurisdiction>
  <purpose
           value="Conditions due to Sickle-cell that can cause painful crisis to be used as exclusions for opioid use recommendations"/>
  <copyright value="© CDC 2016+."/>
  <expansion>
    <timestamp value="2025-01-21T18:47:48.636Z"/>
    <parameter>
      <name value="system-version"/>
      <valueUri
                value="http://snomed.info/sct|http://snomed.info/sct/731000124108/version/20240901"/>
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    <parameter>
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      <valueUri value="http://hl7.org/fhir/sid/icd-10-cm|2024"/>
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    <contains>
      <system value="http://snomed.info/sct"/>
      <code value="417357006"/>
      <display value="Sickling disorder due to hemoglobin S (disorder)"/>
    </contains>
    <contains>
      <system value="http://snomed.info/sct"/>
      <code value="23269001"/>
      <display value="Double heterozygous sickling disorder"/>
    </contains>
    <contains>
      <system value="http://snomed.info/sct"/>
      <code value="25472008"/>
      <display value="Sickle cell-hemoglobin D disease"/>
    </contains>
    <contains>
      <system value="http://snomed.info/sct"/>
      <code value="35434009"/>
      <display value="Sickle cell-hemoglobin C disease"/>
    </contains>
    <contains>
      <system value="http://snomed.info/sct"/>
      <code value="36472007"/>
      <display value="Hemoglobin S-F disease"/>
    </contains>
    <contains>
      <system value="http://snomed.info/sct"/>
      <code value="47024008"/>
      <display value="Sickle cell-hemoglobin E disease"/>
    </contains>
    <contains>
      <system value="http://snomed.info/sct"/>
      <code value="127040003"/>
      <display value="Sickle cell anemia"/>
    </contains>
    <contains>
      <system value="http://snomed.info/sct"/>
      <code value="127041004"/>
      <display value="Sickle cell-beta-thalassemia"/>
    </contains>
    <contains>
      <system value="http://snomed.info/sct"/>
      <code value="127042006"/>
      <display value="Sickle cell beta plus thalassaemia"/>
    </contains>
    <contains>
      <system value="http://snomed.info/sct"/>
      <code value="127043001"/>
      <display value="Sickle cell-beta^0^-thalassemia"/>
    </contains>
    <contains>
      <system value="http://snomed.info/sct"/>
      <code value="127044007"/>
      <display value="Sickle cell-delta beta^0^-thalassemia"/>
    </contains>
    <contains>
      <system value="http://snomed.info/sct"/>
      <code value="127045008"/>
      <display value="Sickle cell anemia with coexistent alpha-thalassemia"/>
    </contains>
    <contains>
      <system value="http://snomed.info/sct"/>
      <code value="127047000"/>
      <display value="Sickle cell-hemoglobin Lepore disease"/>
    </contains>
    <contains>
      <system value="http://snomed.info/sct"/>
      <code value="127048005"/>
      <display value="Sickle cell-Hemoglobin O Arab disease"/>
    </contains>
    <contains>
      <system value="http://snomed.info/sct"/>
      <code value="234391009"/>
      <display value="Sickle cell anemia with high hemoglobin F"/>
    </contains>
    <contains>
      <system value="http://snomed.info/sct"/>
      <code value="416484003"/>
      <display
               value="Sickle cell-hemoglobin E disease with crisis (disorder)"/>
    </contains>
    <contains>
      <system value="http://snomed.info/sct"/>
      <code value="416826005"/>
      <display
               value="Sickle cell-thalassemia disease with crisis (disorder)"/>
    </contains>
    <contains>
      <system value="http://snomed.info/sct"/>
      <code value="417048006"/>
      <display
               value="Sickle cell-thalassemia disease without crisis (disorder)"/>
    </contains>
    <contains>
      <system value="http://snomed.info/sct"/>
      <code value="417279003"/>
      <display value="Hemoglobin S sickling disorder with crisis (disorder)"/>
    </contains>
    <contains>
      <system value="http://snomed.info/sct"/>
      <code value="417425009"/>
      <display value="Hemoglobin SS disease with crisis (disorder)"/>
    </contains>
    <contains>
      <system value="http://snomed.info/sct"/>
      <code value="417517009"/>
      <display
               value="Sickle cell-hemoglobin C disease with crisis (disorder)"/>
    </contains>
    <contains>
      <system value="http://snomed.info/sct"/>
      <code value="417748003"/>
      <display
               value="Sickle cell-hemoglobin D disease with crisis (disorder)"/>
    </contains>
    <contains>
      <system value="http://snomed.info/sct"/>
      <code value="440206000"/>
      <display
               value="Hemoglobin SS disease with vasoocclusive crisis (disorder)"/>
    </contains>
    <contains>
      <system value="http://snomed.info/sct"/>
      <code value="444108000"/>
      <display
               value="Acute sickle cell splenic sequestration crisis (disorder)"/>
    </contains>
    <contains>
      <system value="http://snomed.info/sct"/>
      <code value="783254003"/>
      <display
               value="Hereditary persistence of fetal hemoglobin with sickle cell disease syndrome"/>
    </contains>
    <contains>
      <system value="http://snomed.info/sct"/>
      <code value="1153413001"/>
      <display
               value="Acute sequestration of spleen due to sickle cell thalassemia with crisis (disorder)"/>
    </contains>
    <contains>
      <system value="http://snomed.info/sct"/>
      <code value="1153415008"/>
      <display
               value="Acute splenic sequestration due to sickle cell hemoglobin C disease with crisis"/>
    </contains>
    <contains>
      <system value="http://snomed.info/sct"/>
      <code value="10759351000119103"/>
      <display value="Sickle cell anaemia in mother complicating childbirth"/>
    </contains>
    <contains>
      <system value="http://snomed.info/sct"/>
      <code value="441482006"/>
      <display value="History of sickle cell anaemia"/>
    </contains>
    <contains>
      <system value="http://hl7.org/fhir/sid/icd-10-cm"/>
      <code value="D57"/>
      <display value="Sickle-cell disorders"/>
    </contains>
    <contains>
      <system value="http://hl7.org/fhir/sid/icd-10-cm"/>
      <code value="D57.0"/>
      <display value="Hb-SS disease with crisis"/>
    </contains>
    <contains>
      <system value="http://hl7.org/fhir/sid/icd-10-cm"/>
      <code value="D57.00"/>
      <display value="Hb-SS disease with crisis, unspecified"/>
    </contains>
    <contains>
      <system value="http://hl7.org/fhir/sid/icd-10-cm"/>
      <code value="D57.01"/>
      <display value="Hb-SS disease with acute chest syndrome"/>
    </contains>
    <contains>
      <system value="http://hl7.org/fhir/sid/icd-10-cm"/>
      <code value="D57.02"/>
      <display value="Hb-SS disease with splenic sequestration"/>
    </contains>
    <contains>
      <system value="http://hl7.org/fhir/sid/icd-10-cm"/>
      <code value="D57.03"/>
      <display value="Hb-SS disease with cerebral vascular involvement"/>
    </contains>
    <contains>
      <system value="http://hl7.org/fhir/sid/icd-10-cm"/>
      <code value="D57.04"/>
      <display value="Hb-SS disease with dactylitis"/>
    </contains>
    <contains>
      <system value="http://hl7.org/fhir/sid/icd-10-cm"/>
      <code value="D57.09"/>
      <display
               value="Hb-SS disease with crisis with other specified complication"/>
    </contains>
    <contains>
      <system value="http://hl7.org/fhir/sid/icd-10-cm"/>
      <code value="D57.2"/>
      <display value="Sickle-cell/Hb-C disease"/>
    </contains>
    <contains>
      <system value="http://hl7.org/fhir/sid/icd-10-cm"/>
      <code value="D57.20"/>
      <display value="Sickle-cell/Hb-C disease without crisis"/>
    </contains>
    <contains>
      <system value="http://hl7.org/fhir/sid/icd-10-cm"/>
      <code value="D57.21"/>
      <display value="Sickle-cell/Hb-C disease with crisis"/>
    </contains>
    <contains>
      <system value="http://hl7.org/fhir/sid/icd-10-cm"/>
      <code value="D57.211"/>
      <display value="Sickle-cell/Hb-C disease with acute chest syndrome"/>
    </contains>
    <contains>
      <system value="http://hl7.org/fhir/sid/icd-10-cm"/>
      <code value="D57.212"/>
      <display value="Sickle-cell/Hb-C disease with splenic sequestration"/>
    </contains>
    <contains>
      <system value="http://hl7.org/fhir/sid/icd-10-cm"/>
      <code value="D57.213"/>
      <display
               value="Sickle-cell/Hb-C disease with cerebral vascular involvement"/>
    </contains>
    <contains>
      <system value="http://hl7.org/fhir/sid/icd-10-cm"/>
      <code value="D57.214"/>
      <display value="Sickle-cell/Hb-C disease with dactylitis"/>
    </contains>
    <contains>
      <system value="http://hl7.org/fhir/sid/icd-10-cm"/>
      <code value="D57.218"/>
      <display
               value="Sickle-cell/Hb-C disease with crisis with other specified complication"/>
    </contains>
    <contains>
      <system value="http://hl7.org/fhir/sid/icd-10-cm"/>
      <code value="D57.219"/>
      <display value="Sickle-cell/Hb-C disease with crisis, unspecified"/>
    </contains>
    <contains>
      <system value="http://hl7.org/fhir/sid/icd-10-cm"/>
      <code value="D57.3"/>
      <display value="Sickle-cell trait"/>
    </contains>
    <contains>
      <system value="http://hl7.org/fhir/sid/icd-10-cm"/>
      <code value="D57.4"/>
      <display value="Sickle-cell thalassemia"/>
    </contains>
    <contains>
      <system value="http://hl7.org/fhir/sid/icd-10-cm"/>
      <code value="D57.40"/>
      <display value="Sickle-cell thalassemia without crisis"/>
    </contains>
    <contains>
      <system value="http://hl7.org/fhir/sid/icd-10-cm"/>
      <code value="D57.41"/>
      <display value="Sickle-cell thalassemia, unspecified, with crisis"/>
    </contains>
    <contains>
      <system value="http://hl7.org/fhir/sid/icd-10-cm"/>
      <code value="D57.411"/>
      <display
               value="Sickle-cell thalassemia, unspecified, with acute chest syndrome"/>
    </contains>
    <contains>
      <system value="http://hl7.org/fhir/sid/icd-10-cm"/>
      <code value="D57.412"/>
      <display
               value="Sickle-cell thalassemia, unspecified, with splenic sequestration"/>
    </contains>
    <contains>
      <system value="http://hl7.org/fhir/sid/icd-10-cm"/>
      <code value="D57.413"/>
      <display
               value="Sickle-cell thalassemia, unspecified, with cerebral vascular involvement"/>
    </contains>
    <contains>
      <system value="http://hl7.org/fhir/sid/icd-10-cm"/>
      <code value="D57.414"/>
      <display value="Sickle-cell thalassemia, unspecified, with dactylitis"/>
    </contains>
    <contains>
      <system value="http://hl7.org/fhir/sid/icd-10-cm"/>
      <code value="D57.418"/>
      <display
               value="Sickle-cell thalassemia, unspecified, with crisis with other specified complication"/>
    </contains>
    <contains>
      <system value="http://hl7.org/fhir/sid/icd-10-cm"/>
      <code value="D57.419"/>
      <display value="Sickle-cell thalassemia, unspecified, with crisis"/>
    </contains>
    <contains>
      <system value="http://hl7.org/fhir/sid/icd-10-cm"/>
      <code value="D57.42"/>
      <display value="Sickle-cell thalassemia beta zero without crisis"/>
    </contains>
    <contains>
      <system value="http://hl7.org/fhir/sid/icd-10-cm"/>
      <code value="D57.43"/>
      <display value="Sickle-cell thalassemia beta zero with crisis"/>
    </contains>
    <contains>
      <system value="http://hl7.org/fhir/sid/icd-10-cm"/>
      <code value="D57.431"/>
      <display
               value="Sickle-cell thalassemia beta zero with acute chest syndrome"/>
    </contains>
    <contains>
      <system value="http://hl7.org/fhir/sid/icd-10-cm"/>
      <code value="D57.432"/>
      <display
               value="Sickle-cell thalassemia beta zero with splenic sequestration"/>
    </contains>
    <contains>
      <system value="http://hl7.org/fhir/sid/icd-10-cm"/>
      <code value="D57.433"/>
      <display
               value="Sickle-cell thalassemia beta zero with cerebral vascular involvement"/>
    </contains>
    <contains>
      <system value="http://hl7.org/fhir/sid/icd-10-cm"/>
      <code value="D57.434"/>
      <display value="Sickle-cell thalassemia beta zero with dactylitis"/>
    </contains>
    <contains>
      <system value="http://hl7.org/fhir/sid/icd-10-cm"/>
      <code value="D57.438"/>
      <display
               value="Sickle-cell thalassemia beta zero with crisis with other specified complication"/>
    </contains>
    <contains>
      <system value="http://hl7.org/fhir/sid/icd-10-cm"/>
      <code value="D57.439"/>
      <display
               value="Sickle-cell thalassemia beta zero with crisis, unspecified"/>
    </contains>
    <contains>
      <system value="http://hl7.org/fhir/sid/icd-10-cm"/>
      <code value="D57.44"/>
      <display value="Sickle-cell thalassemia beta plus without crisis"/>
    </contains>
    <contains>
      <system value="http://hl7.org/fhir/sid/icd-10-cm"/>
      <code value="D57.45"/>
      <display value="Sickle-cell thalassemia beta plus with crisis"/>
    </contains>
    <contains>
      <system value="http://hl7.org/fhir/sid/icd-10-cm"/>
      <code value="D57.451"/>
      <display
               value="Sickle-cell thalassemia beta plus with acute chest syndrome"/>
    </contains>
    <contains>
      <system value="http://hl7.org/fhir/sid/icd-10-cm"/>
      <code value="D57.452"/>
      <display
               value="Sickle-cell thalassemia beta plus with splenic sequestration"/>
    </contains>
    <contains>
      <system value="http://hl7.org/fhir/sid/icd-10-cm"/>
      <code value="D57.453"/>
      <display
               value="Sickle-cell thalassemia beta plus with cerebral vascular involvement"/>
    </contains>
    <contains>
      <system value="http://hl7.org/fhir/sid/icd-10-cm"/>
      <code value="D57.454"/>
      <display value="Sickle-cell thalassemia beta plus with dactylitis"/>
    </contains>
    <contains>
      <system value="http://hl7.org/fhir/sid/icd-10-cm"/>
      <code value="D57.458"/>
      <display
               value="Sickle-cell thalassemia beta plus with crisis with other specified complication"/>
    </contains>
    <contains>
      <system value="http://hl7.org/fhir/sid/icd-10-cm"/>
      <code value="D57.459"/>
      <display
               value="Sickle-cell thalassemia beta plus with crisis, unspecified"/>
    </contains>
    <contains>
      <system value="http://hl7.org/fhir/sid/icd-10-cm"/>
      <code value="D57.8"/>
      <display value="Other sickle-cell disorders"/>
    </contains>
    <contains>
      <system value="http://hl7.org/fhir/sid/icd-10-cm"/>
      <code value="D57.80"/>
      <display value="Other sickle-cell disorders without crisis"/>
    </contains>
    <contains>
      <system value="http://hl7.org/fhir/sid/icd-10-cm"/>
      <code value="D57.81"/>
      <display value="Other sickle-cell disorders with crisis"/>
    </contains>
    <contains>
      <system value="http://hl7.org/fhir/sid/icd-10-cm"/>
      <code value="D57.811"/>
      <display value="Other sickle-cell disorders with acute chest syndrome"/>
    </contains>
    <contains>
      <system value="http://hl7.org/fhir/sid/icd-10-cm"/>
      <code value="D57.812"/>
      <display
               value="Other sickle-cell disorders with splenic sequestration"/>
    </contains>
    <contains>
      <system value="http://hl7.org/fhir/sid/icd-10-cm"/>
      <code value="D57.813"/>
      <display
               value="Other sickle-cell disorders with cerebral vascular involvement"/>
    </contains>
    <contains>
      <system value="http://hl7.org/fhir/sid/icd-10-cm"/>
      <code value="D57.814"/>
      <display value="Other sickle-cell disorders with dactylitis"/>
    </contains>
    <contains>
      <system value="http://hl7.org/fhir/sid/icd-10-cm"/>
      <code value="D57.818"/>
      <display
               value="Other sickle-cell disorders with crisis with other specified complication"/>
    </contains>
    <contains>
      <system value="http://hl7.org/fhir/sid/icd-10-cm"/>
      <code value="D57.819"/>
      <display value="Other sickle-cell disorders with crisis, unspecified"/>
    </contains>
  </expansion>
</ValueSet>